Oral Surg Oral Med Oral Pathol. Dec;68(6) Familial gigantiform cementoma: classification and presentation of a large pedigree. Young SK(1). Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents. PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented.

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A diagnosis of a gigantiform cementoma was made. B Reconstructed computed tomography image of familial gigantiform cementoma appearance. This article has been cited by other articles in PMC. In the family reported by Young et al.

Author information Article notes Copyright and License information Disclaimer. Axial CT image showing the radiodense lobular mass surrounded by a radiolucent margin. It is benign, but without intervention it can result in severe disfigurement of the jaw. As a direct consequence, physical deterioration was also found by his parents. During maturation, gigntiform expansion, tooth displacement and progressive opacification occur, all of which are features which distinguish FGC from florid OD.

Gigantiform cementoma

During month follow-up afterwards, the young patient experienced another physical blow of minor-trauma fracture near the femur neck. Published online Mar 7. The feasibility of using fibular flaps was ggantiform out in view of his unfortunate history of frequent lower-extremity fractures.


Therefore, we present a case with a large FGC family history so as to sketch a more detailed portrait of such ailment.

B Preoperative panorex X-ray showed a characteristic radiographic feature of familial gigantiform cementoma FGC with well-circumscribed radiopaque areas involving all quadrants of the jaw, with mandible being more severely damaged. By using this site, you agree to the Terms of Use and Privacy Policy. Open in a separate gigantifom.

The non-expansive ODs are cemsntoma treated when asymptomatic and biopsy is ill-advised owing to the risk of infection. Looking For More References? This page was last edited on 11 Octoberat Macroscopic features of the enucleated specimen.

Gigantiform cementoma in a child. However, extragnathic presentations of FGC in patients have often been neglected, owing in part to rarity of this disease.

Familial Gigantiform Cementoma

Raubenheimer gigantiforrm, David A. The radiological differential diagnosis of a well-defined, expansive mineralized mass in the jawbone includes benign cementoblastoma, osteoma, ossifying fibroma and FGC.

The most famous case is of Novemthree Siahaan who died on September 15,a young Indonesian boy from Batam Island who received medical care in Haulien, Taiwan through a Buddhist missionary from the Tzu Chi Foundationwhich was documented on the Discovery Health Channel.


The disorder is usually not expansile, as is familial gigantiform cementoma. Since then, supplementation of calcium and vitamin D had been prescribed as a method to ameliorate the general calcium metabolism disorder. bigantiform

Gigantiform cementoma in a child

Familial gigantiform cementoma FGC is a distinct and uncommon fibro-cemento-osseous lesion with unknown etiology. Multiquadrant expansile fibro-osseous lesion in a juvenile. According to the latest World Health Organization WHO classification of gigabtiform dysplasias CODsFGC is generally characterized by rapid osseous expansion involving all 4 jaw quadrants with predilection for young patients. You can help Wikipedia by expanding it.

Periapical OD occurs in the anterior mandible and involves the periapical regions of a few incisor teeth, while florid OD is more extensive and can involve the mandible bilaterally or all four jaw quadrants. Benign fibro-osseous diseases of the maxillofacial bones.

Panoramic radiograph showing the highly mineralized lobular lesion in the left maxilla. Head and Neck Tumours.

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